en عمومى General گزارش مورد case report <div style="border: 1.5pt double windowtext; padding: 1pt 4pt 1pt 0in; text-align: justify;"><span style="font-family:Tahoma;"><span style="font-size:12px;"><span style="line-height:normal"><span lang="FR">Adrenocortical carcinoma (ACC) is a rare tumor. It constitutes 0.2% of malignant tumors in children and it is considered ten times rarer than in adults. Patients with predisposing syndromes like Li-Fraumeni or Beckwith-Wiedemann may develop these tumors.</span></span><br> <span style="line-height:normal"><span lang="FR">Clinical symptoms are dominated by endocrine signs, which are present in 90% of cases. The primary cause is virtualization syndrome, which may occur alone or in conjunction with secondary symptoms caused by hypersecretion of adrenal hormones.</span></span><br> <span style="line-height:normal"><span lang="FR">Imaging is indispensable in assessing the malignant nature of the adrenal tumor and its extent. Currently, surgical excision of the tumor is the cornerstone of treatment because its quality often depends on the prognosis of the disease. Adrenocortical carcinoma has a poor prognosis despite treatment, with high chances of recurrence and mortality.</span></span></span></span></div> Adrenocortical Carcinoma, Child, Mortality, Surgical Procedures, Virilism 710 715 http://ijpho.ssu.ac.ir/browse.php?a_code=A-10-1101-1&slc_lang=en&sid=1 HAIF ASSIA HAIF ASSIA a.haif@univ-setif.dz 0000-0001-7382-0219 Yes Department of Pediatric Surgery, University Hospital Center of SETIF, Algeria Department of Pediatric Surgery, University Hospital Center of SETIF, Algeria Djelloul Achouri Djelloul Achouri 0009-0003-6279-0650 No Department of Pediatric Surgery, University Hospital Center of SETIF, Algeria Department of Pediatric Surgery, University Hospital Center of SETIF, Algeria